Hirschsprung’s disease and associated syndrome and malformation -A report of four cases.

نویسندگان

چکیده

Background: Hirschsprung’s disease is a genetic disorder characterized by the absence of ganglion cells in different lengths intestine. It one common causes intestinal obstruction neonates.
 Materials and Methods: The study was carried out from January 2017 to 2020 Department Pathology Tertiary care hospital. biopsy specimens spastic segment colostomy or ileostomy sites were sent for evaluation cells. 
 Results: During carrying we came across two cases that proved who manifested various signs symptoms associated with syndromes malformation neoplasm
 Conclusion: Two neoplasm detected patients during 3-year study.
 Keywords: Hirschsprung's disease, cell, hypertrophic nerve fiber, malformation, neoplasm, syndrome.

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ژورنال

عنوان ژورنال: Indian Journal of Case Reports

سال: 2022

ISSN: ['2454-129X', '2454-1303']

DOI: https://doi.org/10.32677/ijcr.v8i1.3212